Article
Bull’s Eye Maculopathy in Cone Dystrophy
Retinal analysis of a 12-year-old boy with complaint of diminution of vision and nystagmus
13 September 2023
![Bull’s Eye Maculopathy in Cone Dystrophy True color ultra-widefield fundus imaging True color ultra-widefield fundus imaging]({"xsmall":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.100.75.24,84,1610,1274.file/c4_agrawal_1.jpg","small":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.360.270.24,84,1610,1274.file/c4_agrawal_1.jpg","medium":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.768.576.24,84,1610,1274.file/c4_agrawal_1.jpg","large":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1024.768.24,84,1610,1274.file/c4_agrawal_1.jpg","xlarge":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1280.960.24,84,1610,1274.file/c4_agrawal_1.jpg","xxlarge":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1440.1080.24,84,1610,1274.file/c4_agrawal_1.jpg","max":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1586.1190.24,84,1610,1274.file/c4_agrawal_1.jpg"})
Bull’s Eye Maculopathy in Cone Dystrophy
![Bull’s Eye Maculopathy in Cone Dystrophy True color ultra-widefield fundus imaging True color ultra-widefield fundus imaging]({"xsmall":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.100.82.file/c4_agrawal_1.jpg","small":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.360.294.file/c4_agrawal_1.jpg","medium":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.768.627.file/c4_agrawal_1.jpg","large":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1024.836.file/c4_agrawal_1.jpg","xlarge":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1280.1045.file/c4_agrawal_1.jpg","xxlarge":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original.image_file.1440.1175.file/c4_agrawal_1.jpg","max":"https://www.zeiss.com/content/dam/med-hcp/international/campaigns/clarus-library/dr-vishay-agrawal-/bull_s-eye-maculopathy-in-cone-dystrophy/c4_agrawal_1.jpg/_jcr_content/renditions/original./c4_agrawal_1.jpg"})
Figure 1
True color ultra-widefield fundus imaging helped in detecting Bull’s Eye Maculopathy suggesting Cone Dystrophy. On widefield imaging it appeared like an eye on macula due to nystagmus. Prognosis ranges from benign to total visual loss by late middle age.